European Journal of Cardio-Thoracic Surgery, Vol 1, 180-182, Copyright © 1987 by European Association for Cardio-thoracic Surgery
Partially unroofed coronary sinus associated with tricuspid atresia. An important associated lesion in the Fontan operation
R Matsuwaka, T Tomokuni, S Ishikawa, F Watanabe, T Matsushita and H Matsuda
Division of Cardiovascular Surgery, Osaka University Medical School, Japan.
A case of tricuspid atresia associated with partially unroofed coronary
sinus following a Fontan operation is described. A 4-year-old boy with
tricuspid atresia showed persistent arterial desaturation immediately after
a modified Fontan operation. At reoperation on the next day, a partially
unroofed coronary sinus was recognized and repaired through a left
atriotomy. Although uncommon, this associated anomaly should be kept in
mind even in the absence of a persistent left superior vena cava and should
be suspected if arterial desaturation occurs after a modified Fontan
operation.