European Journal of Cardio-Thoracic Surgery, Vol 2, 58-60, Copyright © 1988 by European Association for Cardio-thoracic Surgery
Intravenous leiomyomatosis: a rare cause of right sided cardiac obstruction
JM Rosenberg, MA Marvasti, A Obeid, LW Johnson and M Bonaventura
Department of Surgery, SUNY Health Science Center, Syracuse.
Intravenous leiomyomatosis involving the right side of the heart is an
unusual cause of outflow obstruction. Evaluation of the patient should be
directed not only at intracardiac chambers but also at the inferior vena
cava. This should include angiography and MRI or CAT scanning.
Echocardiography is an important contributory investigation. Surgical
therapy should be directed at complete removal of the tumor as recurrence
has been reported if a less than complete resection has been performed.
Hormonal manipulation has been attempted with variable results.