European Journal of Cardio-Thoracic Surgery, Vol 2, 405-409, Copyright © 1988 by European Association for Cardio-thoracic Surgery
Late results of total correction of tetralogy of Fallot in adults
TK Kaul, R al Khadimi and JL Mercer
Regional Adult Cardiothoracic Unit, Broadgreen Hospital, Liverpool, UK.
Between 1966 and 1986, 30 patients underwent total correction of the
tetralogy of Fallot. Preoperative presenting features were: dyspnoea on
exertion, clubbing, cyanosis and polycythaemia. Twenty-six patients had one
or more palliative procedures prior to definitive repair. Preoperatively,
all patients had a significant gradient across the right ventricular
outflow tract (mean gradient 70 +/- 46 mmHg). Peak right ventricle to left
ventricle systolic pressure ratio (pRV/LV) was 0.9 +/- 0.2. A functioning
Blalock Taussig shunt was ligated in 11 patients prior to the institution
of cardiopulmonary bypass. All patients had a patch closure of the
ventricular septal defect. An additional muscle bundle resection from the
right ventricular outflow tract was performed in 15, pulmonary valvotomy in
6 and enlargement of the right ventricular outflow tract in 2 patients.
There was a significant fall in pRV/LV ratio postoperatively (P less than
0.05). There were 3 early and 2 late deaths. Mild right ventricular outflow
tract obstruction has persisted in all survivors. Four patients have
remained on antiarrhythmic drugs. Long term results after definitive repair
were satisfactory in this group of adult patients who have survived due to
palliative procedures performed during childhood.