European Journal of Cardio-Thoracic Surgery, Vol 5, 608-609, Copyright © 1991 by European Association for Cardio-thoracic Surgery
Congenital aortic regurgitation caused by absence of the right coronary cusp
AH Cromme-Dijkhuis and JJ Meuzelaar
Department of Paediatric Cardiology, University Hospital, Groningen, The Netherlands.
We describe a patient with congenital aortic regurgitation, well documented
from the age of 1 month. Surgery was performed at the age of 7 years, when
echocardiography showed progressive dilatation of the left ventricle with
decreasing shortening fraction. Inspection of the valve during the
operation showed a basically tricuspid valve, but with a rudimentary right
coronary cusp. At histological examination, myxoid dysplasia was found in
all the cusps. An aortic homograft was inserted and the left ventricular
internal dimensions returned to normal within 3 months after the operation.