European Journal of Cardio-Thoracic Surgery, Vol 6, 625-626, Copyright © 1992 by European Association for Cardio-thoracic Surgery
Aortic valve replacement in cardiac ochronosis
YI Kim and W Daenen
Department of Cardiac Surgery, University Hospital, Gasthuisberg, Leuven, Belgium.
Two patients with generalized ochronosis developed cardiovascular symptoms
related to cardiac ochronosis with aortic valvular stenosis. One patient
with a transvalvular pressure gradient of 150 mm Hg underwent emergency
aortic valve replacement. The other patient with a transvalvular pressure
gradient of 96 mm Hg underwent successful elective aortic valve
replacement. Cardiac ochronosis is a rare disease that might be
encountered, with the typical signs, during an elective, planned cardiac
operation. The most frequent presenting feature of this disease seems to be
aortic valvular stenosis.