European Journal of Cardio-Thoracic Surgery, Vol 8, 391-392, Copyright © 1994 by European Association for Cardio-thoracic Surgery
Surgical repair of transposition of great arteries and total anomalous pulmonary venous return to the coronary sinus (TGA with TAPVR)
B Gontijo, F Fantini, M Barbosa, MV Gomes, C Gutierrez and M Vrandecic
Biocor Institute, Biocor Hospital de Doencas Cardiovasculares Ltda., Belo Horizonte, MG, Brazil.
The association of transposition of the great arteries (TGA) and total
anomalous pulmonary venous return (TAPVR) is very rare; we report one case
of this malformation with an intracardiac type of TAPVR draining into the
coronary sinus. The surgical repair was performed directing the coronary
sinus blood flow to the tricuspid valve. The proximity of the anatomical
structures allowed an intra-atrial patch repair similar to a modified
Mustard procedure. In the postoperative period the child developed low
cardiac output for 2 days, requiring inotropic support and mechanical
ventilation. Her recovery was otherwise uneventful. The postoperative
echocardiogram showed an intact repair with perfect flow through the patch
from the pulmonary veins to the right ventricle. Almost 2 years after
surgery, the patient underwent cardiac catheterization that showed
integrity of the surgical repair with normal pressures in all heart
chambers. To our knowledge this is the first report in the medical
literature of surgical treatment of this association.